Spinocerebellar Atrophy Type-3 with Chiari Malformation in a Young Man: A Case Report

  • Sepideh Paybast ORCID Neurology Department, BoualiSina Hospital, Qazvin University of Medical Sciences, Qazvin, Iran.
  • Mohsen Koosha ORCID Neurosurgery Department, Imam Hossin Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran
  • Dina Motamedi ORCID Mail Neurology Department Ghods Hospital, Kurdistan University of Medical Sciences, Sannandaj, Iran
  • Arman Habibi Neurology Department, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran
Ataxia, Case Reports, Chiari Malformation, Spinocerebellar Atrophy


Introduction: Chiari malformations are a group of congenital anomalies which involve the hindbrain and the cervical spinal canal. Case presentation: Here, we describe a patient who presented with acute diplopia and gait unsteadiness which was first deigned with Chiari malformation type-1. However due to progression of the ataxia the full neurologic evaluation was considered which established the diagnosis of spinocerebellar ataxia type 3 (Machado-Joseph-Disease). Conclusion: We aim to highlight the importance of careful examination in order to avoid misdiagnosis of even rare diseases.


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How to Cite
Paybast S, Koosha M, Motamedi D, Habibi A. Spinocerebellar Atrophy Type-3 with Chiari Malformation in a Young Man: A Case Report. Adv J Emerg Med. 4(2):e30.
Case (report / study)